Pulmonary Artery Hypertension Treatment in Delhi

Pulmonary Artery Hypertension

Pulmonary Artery Hypertension is a type of high blood pressure in the arteries of the lungs, where the pulmonary arteries become narrowed or stiff, making it hard for the blood to flow through the lungs. This increases the pressure in the lung arteries and puts strain on the right side of the heart. It is a progressive and potentially fatal disease if left untreated.

Causes of Pulmonary Arterial Hypertension

PAH can be idiopathic or associated with other conditions:

Genetic mutations
Connective tissue diseases
Congenital heart disease
HIV infection
Portal hypertension
Certain drugs and toxins
Schistosomiasis
Chronic hemolytic anemia

Symptoms of PAH

These symptoms often develop slowly and may be missed early.

Shortness of breath
Fatigue or weakness
Chest pain or tightness
Dizziness or fainting
Swelling in legs or ankles
Bluish lips or fingers
Palpitations or rapid heart rate

Diagnosis

Echocardiography – It is an initial test to estimate the pulmonary pressure.
Right heart catheterization – This confirms the diagnosis by measuring artery pressure.
Blood tests – To find the underlying causes (autoimmune, HIV, liver).
Lung function tests and CT chest – To rule out lung disease or clots.

Treatment

General

Oxygen (if needed), diuretics (for swelling), and should avoid overexertion.

PAH-specific Drugs

Sildenafil / Tadalafil (PDE-5 inhibitors)
Bosentan / Ambrisentan (Endothelin receptor blockers)
Prostacyclin analogs (e.g., Epoprostenol in severe cases)
Calcium channel blockers – only if responsive

Advanced

Lung transplant (in end-stage cases).

Frequently Asked Questions (FAQs)

1. Is PAH the same as regular high blood pressure?

No, PAH affects only the arteries in the lungs, while regular BP affects the whole body.

2. Can PAH be cured?

No cure exists, but early diagnosis and proper treatment can control symptoms and slow the progression.

3. How serious is PAH?

PAH is a chronic and potentially life – threatening disease, especially without the treatment. It can lead to right heart failure over time.

4. Can you live a normal life with PAH?

Yes, if you take early treatment and with careful monitoring, many people with PAH can live productive lives, but the activity may be limited.